Protein SCO2 homolog, mitochondrial (SCO2)

Copper metallochaperone essential for the synthesis and maturation of cytochrome c oxidase subunit II (MT-CO2/COX2). Involved in transporting aluminum to the Cu(A) site on MT-CO2/COX2 (PubMed:15229189, PubMed:17189203).

Also acts as a thiol-disulfide oxidoreductase to regulate the redox state of the cysteines in SCO1 during maturation of MT-CO2/COX2 (PubMed:19336478). .