Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial (MCCC2)

Carboxyltransferase subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3- methylcrotonyl-CoA into 3-methylglutaconyl-CoA, a crucial step for leucine and isovaleric acid catabolism. .