Probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial (DHTKD1)

The 2-oxoglutarate dehydrogenase complex catalyzes the overall conversion of 2-oxoglutarate into succinyl-CoA and CO(2). It contains multiple copies of three enzymatic components: 2- oxoglutarate dehydrogenase (E1), dihydrolipoamide succinyltransferase (E2) and lipoamide dehydrogenase (E3) (By similarity).

. .