BCS1L Antibodies

AND BCS1L ELISA kits, BCS1L Proteins

Many biological assays use antibodies to detect BCS1L, such as Western Blot (WB), ELISA, Flow Cytometry, Immunocytochemistry (IHC). These antibodies can be polyclonal or monoclonal, and react with BCS1L in Human, Mouse, Rat, and many other animal samples. Boster Bio use mainly mouse and rabbit to develop BCS1L antibodies...

We validate the specificity of these antibodies to BCS1L by testing them on tissues known to express BCS1L positively and negatively. Browse below to find the BCS1L antibody that suites your experiment. We have 3 of these antibodies and many publications and validation images.

If you cannot find antibodies that fit your needs, contact us for making custom antibodies. We have a full suite of custom antibody services covering from research to diagnostic and therapeutic applications.

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BCS1L Infographic by Boster Bio

All BCS1L Products

Product

Figures

Specificity

Applications

Price

Anti-Mitochondrial chaperone BCS1 BCS1L Antibody

Human, Mouse, Rat

IF, IHC, ICC, WB

$405
Cat # A04885
100ul

BCS1L (NM_004328) Human Recombinant Protein

$1249
Cat # PROTQ9Y276
20 µg

BCS1L (NM_004328) Human Over-expression Lysate

Human

$628
Cat # LS000617
100 µg

BCS1L Overview

Facts about Mitochondrial chaperone BCS1.

BCS1L 3D structure. Source: alphafold

Mitochondrial chaperone BCS1 (BCS1L)

Chaperone necessary for the assembly of mitochondrial respiratory chain complex III. Plays an essential part in the maintenance of mitochondrial tubular networks, respiratory chain formation and assembly of the LETM1 complicated.

Gene Information

Human
Gene Name:	BCS1L
Uniprot:	Q9Y276
Entrez:	617

Family

Belongs to:

AAA ATPase family

Alternative Names

BCS; BCS1 (yeast homolog)-like; BCS1; BCS1-like (S. cerevisiae); BCS1-like (yeast); BCS1-like protein; BJSGRACILE; FLNMS; h-BCS; h-BCS1; mitochondrial chaperone BCS1; mitochondrial complex III assembly; PTD

Molecular Weight

Mass (kDA):
47.534 kDA

Genomic Context


Human

Location:	2q35
Sequence:	2; NC_000002.12 (218659683..218663443)

Tissue Specificity

Ubiquitous.

Subcellular Localizations

Mitochondrion inner membrane; Single-pass membrane protein.

Diseases

Ubiquinone Dehydrogenase
Gracile Syndrome (disorder)
Mitochondrial Diseases
Cholestasis
Acidosis, Lactic
Fetal Growth Retardation
Acidosis
Liver Diseases
Iron Overload
Aminoaciduria
Liver Dysfunction
Liver Failure

Liver Cirrhosis
Growth Retardation
Aortic Aneurysm, Abdominal
Inborn Errors Of Metabolism
Hemosiderosis
Encephalopathies
Metabolic Diseases

Pathways

Pathogenesis
Respiratory Chain Complex Iii Assembly
Transport
Translation
Electron Transport
Cell Death
Oxidative Phosphorylation

Membrane Fusion
Protein Unfolding

PTMs

Oxidation

For details, visit:
bosterbio.com/bosterbio-gene-info-cards/BCS1L

References

PMID: 9878253 by Petruzzella V., et al. Identification and characterization of human cDNAs specific to BCS1, PET112, SCO1, COX15, and COX11, five genes involved in the formation and function of the mitochondrial respiratory chain.

PMID: 11528392 by de Lonlay P., et al. A mutant mitochondrial respiratory chain assembly protein causes complex III deficiency in patients with tubulopathy, encephalopathy and liver failure.