PCCB Antibodies

AND PCCB ELISA kits, PCCB Proteins

Many biological assays use antibodies to detect PCCB, such as Western Blot (WB), ELISA, Flow Cytometry, Immunocytochemistry (IHC). These antibodies can be polyclonal or monoclonal, and react with PCCB in Human, Mouse, Rat, and many other animal samples. Boster Bio use mainly mouse and rabbit to develop PCCB antibodies...

We validate the specificity of these antibodies to PCCB by testing them on tissues known to express PCCB positively and negatively. Browse below to find the PCCB antibody that suites your experiment. We have 2 of these antibodies and many publications and validation images.

If you cannot find antibodies that fit your needs, contact us for making custom antibodies. We have a full suite of custom antibody services covering from research to diagnostic and therapeutic applications.

Previous: CBLIF Next: PCDH1

PCCB Infographic by Boster Bio

All PCCB Products

Product

Figures

Specificity

Applications

Price

Anti-PCCB Antibody

Human, Mouse

IF, WB

$405
Cat # A04326
100ul

Anti-PCCB Antibody Picoband™

Human, Mouse, Rat

ELISA, Flow Cytometry, IHC, WB

$370
Cat # A04326-1
100 µg/vial

PCCB Overview

Facts about Propionyl-CoA carboxylase beta chain, mitochondrial.

PCCB 3D structure. Source: alphafold

Propionyl-CoA carboxylase beta chain, mitochondrial (PCCB)

Gene Information

Human
Gene Name:	PCCB
Uniprot:	P05166
Entrez:	5096

Family

Belongs to:

AccD/PCCB family

Alternative Names

beta polypeptide; mitochondrial; propionyl CoA carboxylase, beta polypeptide

Molecular Weight

Mass (kDA):
58.216 kDA

Genomic Context


Human

Location:	3q22.3
Sequence:	3; NC_000003.12 (136250325..136330171)

Subcellular Localizations

Mitochondrion matrix.

Diseases

Propionic Acidemia
Acidemia
Inborn Errors Of Metabolism
Metabolic Diseases
Metabolic Acidosis
Acidosis
Comatose
Hyperammonemia
Cardiovascular Diseases
Mutation, Out-of-frame
Propionic Acidemia, Type Ii

Methylmalonic Acidemia
Muscle Hypotonia
Inflammation
Lethargy
Congenital Heart Defects

Interacting Proteins

PCCA

Pathways

Translation
Blood Coagulation
Fermentation
Coagulation
Ammonia Oxidation
Tropism

Hemostasis

PTMs

Carboxylation

Biotinylation

Oxidation

Research Areas

Stem Cell Markers

For details, visit:
bosterbio.com/bosterbio-gene-info-cards/PCCB

References

PMID: 8188292 by Lamhonwah A.-M., et al. Correction of the metabolic defect in propionic acidemia fibroblasts by microinjection of a full-length cDNA or RNA transcript encoding the propionyl-CoA carboxylase beta subunit.

PMID: 8225321 by Ohura T., et al. The molecular defect in propionic acidemia: exon skipping caused by an 8-bp deletion from an intron in the PCCB allele.