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- Table of Contents
Facts about Malonyl-CoA decarboxylase, mitochondrial.
In peroxisomes it may be involved in degrading intraperoxisomal malonyl-CoA, which is generated by the peroxisomal beta-oxidation of odd chain-length dicarboxylic fatty acids. Plays a role in the metabolic balance between sugar and lipid oxidation in muscle independent of alterations in insulin signaling.
Human | |
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Gene Name: | MLYCD |
Uniprot: | O95822 |
Entrez: | 23417 |
Belongs to: |
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No superfamily |
EC 4.1.1.9; hMCD; malonyl-CoA decarboxylase; malonyl-CoA decarboxylase, mitochondrial; MCDmalonyl coenzyme A decarboxylase; MGC59795
Mass (kDA):
55.003 kDA
Human | |
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Location: | 16q23.3 |
Sequence: | 16; NC_000016.10 (83899115..83927031) |
Expressed in fibroblasts and hepatoblastoma cells (at protein level). Expressed strongly in heart, liver, skeletal muscle, kidney and pancreas. Expressed in myotubes. Expressed weakly in brain, placenta, spleen, thymus, testis, ovary and small intestine.
Cytoplasm. Mitochondrion matrix. Peroxisome. Peroxisome matrix. Enzymatically active in all three subcellular compartments.
PMID: 10417274 by FitzPatrick D.R., et al. The molecular basis of malonyl-CoA decarboxylase deficiency.
PMID: 10455107 by Sacksteder K.A., et al. MCD encodes peroxisomal and cytoplasmic forms of malonyl-CoA decarboxylase and is mutated in malonyl-CoA decarboxylase deficiency.